[1]张 坤,薛绛宇,白卫星,等.Klippel- Trenaunay综合征伴脊髓动-静脉瘘、蛛网膜下腔出血1例并文献复习 [J].介入放射学杂志,2018,27(02):175-177.
 ZHANG Kun,XUE Jiangyu,BAI Weixing,et al.Klippel- Trenaunay syndrome complicated by spinal arteriovenous fistula and subarachnoid hemorrhage: report of one case with literature review[J].journal interventional radiology,2018,27(02):175-177.
点击复制

Klippel- Trenaunay综合征伴脊髓动-静脉瘘、蛛网膜下腔出血1例并文献复习
()

PDF下载中关闭

分享到:

《介入放射学杂志》[ISSN:1008-794X/CN:31-1796/R]

卷:
27
期数:
2018年02期
页码:
175-177
栏目:
临床研究
出版日期:
2018-02-25

文章信息/Info

Title:
Klippel- Trenaunay syndrome complicated by spinal arteriovenous fistula and subarachnoid hemorrhage: report of one case with literature review
作者:
张 坤 薛绛宇 白卫星 李天晓 赵同源 贺迎坤 韩冰莎 许岗勤
Author(s):
ZHANG Kun XUE Jiangyu BAI Weixing LI Tianxiao ZHAO Tongyuan HE Yingkun HAN Bingsha XU Gangqin
Department of Interventional Radiology, Henan Provincial People’s Hospital, Zhengzhou, Henan Province 450003, China
关键词:
【关键词】 Klippel- Trenaunay综合征 脊髓动-静脉瘘 蛛网膜下腔出血 介入治疗
文献标志码:
A
摘要:
【摘要】 目的 报道介入治疗Klippel- Trenaunay 综合征(KTS)伴脊髓动-静脉瘘、蛛网膜下腔出血1 例,结合文献复习探讨介入治疗该疾病的方法和临床价值。方法 1 例女性儿童患者,术前临床表现及影像学检查确诊KTS伴脊髓动-静脉瘘、蛛网膜下腔出血,诊断明确后行脊髓动-静脉瘘栓塞术。结果 手术均顺利进行,术后患者临床症状逐渐消失,无并发症发生。结论 介入治疗KTS伴脊髓动-静脉瘘、蛛网膜下腔出血微创、安全、疗效确切。

参考文献/References:


[1] Forbes N, Walwyn M, Rao G, et al. Klippel- Trenaunay syndrome[J]. West Indian Med J, 2013, 62: 254- 256.
[2] Frasier K, Giangola G, Rosen R, et al. Endovascular radiofrequency ablation: a novel treatment of venous insufficiency in Klippel- Trenaunay patients[J]. J Vasc Surg, 2008, 47: 1339- 45.
[3] 马永杰, 李桂林, 卞立松, 等. 颅颈交界区硬脊膜动静脉瘘及髓周动静脉瘘各一例并文献复习[J]. 中国脑血管病杂志,2016, 13: 146- 149.
[4] Kihiczak GG, Meine JG, Schwartz RA, et al. Klippel- Trenaunay syndrome: a multisystem disorder possibly resulting from a pathogenic gene for vascular and tissue overgrowth[J]. Int J Dermatol, 2006, 45: 883- 890.
[5] 李开成, 罗济程, 余 强, 等. Klippel- Trenaunay综合征动脉DSA检查的影像探讨[J]. 介入放射学杂志, 2008, 17: 84- 85.
[6] Dimopoulos A, Sicko RJ, Kay DM, et al. Copy number variants in a population- based investigation of Klippel- Trenaunay syndrome[J]. Am J Med Genet A, 2017, 173: 352- 359.
[7] Apostolova M, Nasser S, Kodsi S. A rare case of spinal dural arteriovenous fistula[J]. Neurol Int, 2012, 4: 87- 89.
[8] Rodesch G, Lasjaunias P. Spinal cord arteriovenous shunts: from imaging to management[J]. Eur J Radiol, 2003, 46: 221- 232.
[9] 解玲玲, 孙成建, 王彦华, 等. 血管内栓塞治疗硬脊膜动静脉瘘临床结果[J]. 介入放射学杂志, 2015, 24: 185- 187.
[10] Hartman J, Rabinstein AA. Can we rule out a spinal arteriovenous fistula using only MRI? Yes, we can[J]. Neurology, 2012, 79: 15- 16.
[11] 葛许华, 于德华, 张含之, 等. 13例硬脊膜动静脉瘘的临床特征与误诊分析[J]. 中风与神经疾病杂志, 2017, 34, 157- 160.
[12] Jeng Y, Chen DY, Hsu HL, et al. Spinal dural arteriovenous fistula: imaging features and its mimics[J]. Korean J Radiol, 2015, 16: 1119- 1131.
[13] Reinges MH, Thron A, Mull M, et al. Dural arteriovenous fistulae at the foramen magnum[J]. J Neurol, 2001, 248: 197- 203.
[14] Spetzler RF, Wilson CB, Weinstein P, et al. Normal perfusion pressure breakthrough theory[J]. Clin Neurosurg, 1978, 25:651- 672.

备注/Memo

备注/Memo:
(收稿日期:2017-03-13)
(本文编辑:俞瑞纲)
更新日期/Last Update: 2018-02-24