[1]李 艳,吕传剑,吴学军,等. 遗传性出血性毛细血管扩张症累及肝脏的CT及DSA表现[J].介入放射学杂志,2013,(10):854-857.
　LI Yan,LV Chuan? jian,WU Xue? jun,et al. Hepatic involvement of hereditary hemorrhagic telangiectasia： its imaging findings on CT and DSA[J].journal interventional radiology,2013,(10):854-857.
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 遗传性出血性毛细血管扩张症累及肝脏的CT及DSA表现 ()

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《介入放射学杂志》[ISSN:1008-794X/CN:31-1796/R]

卷:
期数:
2013年10期
页码:
854-857
栏目:
临床研究
出版日期:
2013-10-15

文章信息/Info

Title:
 Hepatic involvement of hereditary hemorrhagic telangiectasia： its imaging findings on CT and DSA
作者:
 李 艳;  吕传剑;  吴学军;  吴青霞;  孙明华;  葛英辉
Author(s):
 LI Yan;  LV Chuan?蛳 jian;  WU Xue?蛳 jun;  WU Qing?蛳 xia;  SUN Ming?蛳 hua;  GE Ying?蛳 hui.
 Department of Radiology， Henan Provincal People’s Hospital， Zhengzhou 450003， China
关键词:
 ; 【关键词】 遗传性出血性毛细血管扩张症;  肝脏;  计算机断层扫描;  血管造影
文献标志码:
A
摘要:
 【摘要】 目的 探讨遗传性出血性毛细血管扩张症（hereditary hemorrhagic telangiectasia，HHT）累及肝脏的CT和DSA表现。方法 回顾性分析2005年9月至2012年10月6例HHT累及肝脏患者的临床及CT、DSA影像学资料。结果 CT增强表现为动脉期肝动脉及其分支迂曲扩张，肝静脉和门静脉早显、增粗。此期肝内见多发大小不等的灶状、小片状强化。门脉期部分病灶持续强化，同时肝实质强化，肝动脉密度减低，门静脉及肝静脉显示更清晰。CTA显示肝动脉变异。DSA表现为肝动脉及其分支明显增粗、迂曲；肝实质呈弥漫性团块状染色，肝静脉提前显影，门静脉主干及肝内分支增粗，还可见肝动脉变异以及肠系膜上动脉窃血。结论 CT增强及DSA在HHT肝脏受累有特征性表现，对HHT的诊断具有重要价值。

参考文献/References:

 ［1］ Piantanida M， Buscarini E， Dellavecchia C， et al. Hereditary haemorrhagic telangiectasia with extensive liver involvement is not caused by either HHT1 or HHT2［J］. J Med Genet， 1996， 33： 441 ?蛳 443.
［2］ Alonso?蛳 Trece?觡o JL， Alonso?蛳 Casta?觡eira I， Escapa?蛳 Garrachón JM， et al. Nasa1 closure as definitive treatment for epistaxis in Rendu?蛳 Osler?蛳 Weber disease［J］. Acta Otorrinolaringol Esp， 2008， 59： 420 ?蛳 423.
［3］ Memeo M， Stabile Ianora AA， Scardapane A， et al. Hepatic involvement in hereditary hemorrhagic telangiectasia： CT findings［J］. Abdom Imaging， 2004， 29： 211 ?蛳 220.
［4］ Shovlin CL， Guttmacher AE， Buscarini E， et al. Diagnostic criteria for hereditary hemorrhagic telangiectasia（Rendu?蛳 Osler?蛳 Weber syndrome）［J］. Am J Med Genet， 2000， 91： 66 ?蛳 67.
［5］ Cymerman U， Vera S， Pece?蛳 Barbara N， et al. Identification of hereditary hemorrhagic telangiectasia type 1 in newborns by protein expression and mutation analysis of endoglin［J］. Pediatr Res， 2000， 47： 24 ?蛳 35.
［6］ 卢 川， 刘作勤． 遗传性出血性毛细血管扩张症的影像学诊断和介入治疗研究进展［J］． 介入放射学杂志， 2008， 17： 290 ?蛳 293．
［7］ 秦 玲， 刘 珂， 赵小强， 等． 遗传性出血性毛细血管扩张症的临床研究［J］． 中国当代医药， 2012， 19： 55 ?蛳 56．
［8］ Kuehl HK， Caselitz M， Hasenkamp S， et al. Hepatic manifestation is associated with ALK1 in hereditary hemorrhagic telangiectasia： identification of five novel ALK1 and one novel ENG mutations［J］. Hum Mutat， 2005， 25： 320.
［9］ 连庆峰， 刘学静， 闫 欣， 等． MSCT血管成像对肝脏遗传性出血性毛细血管扩张症的诊断［J］． 实用放射学杂志， 2011， 27： 1180 ?蛳 1182．
［10］ Lanora AA， Memeo M， Sabba C， et al. Hereditary hemorrhagic telangieetasia： multi?蛳 detector row helical CT assessment of hepatic involvement［J］. Radiology， 2004， 230： 250 ?蛳 259.
［11］ Siddiki H， Doherty MG， Fletcher JG， et al. Abdominal findings in hereditary hemorrhagic telangiectasia： pictorial essay on 2D and 3D findings with isotropic multiphase CT［J］. Radiographics， 2008， 28： 171 ?蛳 184. 

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备注/Memo

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 （收稿日期：２０１3-０4-2０）
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